Oman Journal of Ophthalmology

CLINICAL QUIZ
Year
: 2019  |  Volume : 12  |  Issue : 2  |  Page : 141-

The golden ring


Simar Rajan Singh, Sonam Yangzes, Jagat Ram 
 Department of Ophthalmology, Advanced Eye Centre, Post Graduate Institute of Medical Education and Research, Chandigarh, India

Correspondence Address:
Dr. Jagat Ram
Department of Ophthalmology, Advanced Eye Centre, Post Graduate Institute of Medical Education and Research, Sector 12, Chandigarh
India




How to cite this article:
Singh SR, Yangzes S, Ram J. The golden ring.Oman J Ophthalmol 2019;12:141-141


How to cite this URL:
Singh SR, Yangzes S, Ram J. The golden ring. Oman J Ophthalmol [serial online] 2019 [cited 2020 Nov 28 ];12:141-141
Available from: https://www.ojoonline.org/text.asp?2019/12/2/141/259688


Full Text



 Case Presentation



Afemale in her mid-20s presented to the ophthalmologist with low vision in both eyes since childhood. On examination, she had a best-corrected visual acuity of 20/80 in the right eye with 17.00 Ds and 20/40 in the left eye with 14.00 Ds. Intraocular pressures were normal. On close inspection, both eyes [Figure 1] (Panel A – right eye, Panel B – left eye) had thick lenses with 360° golden ring around the lens on retroillumination. Posterior segment examination was unremarkable. Systemic examination revealed a short stature, brachydactyly, and joint stiffness.{Figure 1}

 Questions



What is the ocular diagnosis?

Subluxated lensMicrospherophakiaKeratoconusLenticonus

Which of the following syndromes are most commonly associated with this abnormality?

Marfan's syndromeAlport syndromeWeill–Marchesani syndromeEhlers–Danlos syndrome

What is the best surgical management for this patient?

Clear lens extraction with intraocular lens implantationLaser-assisted in situ keratomileusisPenetrating keratoplastyImplantable Collamer Lens

 View Answer

 Answers



bca

 Case Description



This is a case of microspherophakia with Weill–Marchesani Syndrome. Microspherophakia is a lenticular abnormality in which the existing zonules lack tension that directly contributes to the presence of a small spherical lens.[1] The laxity of the zonules may lead to anterior subluxation of the lens which can cause uneven shallowing of the anterior chamber, sometimes even leading to raised intraocular pressure.[2],[3] In a dilated pupil, the margin of the crystalline lens can be seen as a golden ring on retroillumination. This condition must be ruled out in all cases of high myopic refractive error with a dilated slit lamp examination. Surgical intervention may be required in cases of high refractive error, lens subluxation or glaucoma. This patient was managed with sequential clear lens extraction with in-the-bag intraocular lens implantation and capsular tension segments.[4] She maintains an unaided vision of 20/30 in both eyes after 1-year follow-up.

Declaration of patient consent

The authors certify that they have obtained all appropriate patient consent forms. In the form the patient(s) has/have given his/her/their consent for his/her/their images and other clinical information to be reported in the journal. The patients understand that their names and initials will not be published and due efforts will be made to conceal their identity, but anonymity cannot be guaranteed.

Financial support and sponsorship

Nil.

Conflicts of interest

There are no conflicts of interest.